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Date Published: 28/10/2025
Abstract Views: 26
Views PDF: 10
DOI: 10.56535/jmpm.v50i8.985
Issue
Vol. 50 No. 8 (2025): JOURNAL OF MILITARY PHARMACO-MEDICINE No.8 - 2025
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Articles
How to Cite
Nguyễn Trần, N. V., Nguyen, V. C., Truong Minh, T., & Dang Thanh, T. A. (2025). URETEROPELVIC JUNCTION OBSTRUCTION IN PATIENTS WITH HERLYN-WERNER-WUNDERLICH SYNDROME: A CLINICAL CASE REPORT. Journal of Military Pharmaco-medicine, 50(8), 208-215. https://doi.org/10.56535/jmpm.v50i8.985

URETEROPELVIC JUNCTION OBSTRUCTION IN PATIENTS WITH HERLYN-WERNER-WUNDERLICH SYNDROME: A CLINICAL CASE REPORT

Nữ Vương Nguyễn Trần1, , Viet Cuong Nguyen1, Thuong Truong Minh1, Tu Anh Dang Thanh1
1 Bệnh viện Quân y 175

Main Article Content

Abstract

Objectives: To report a case of ureteropelvic junction obstruction (UPJO) in a solitary kidney in a patient with Herlyn-Werner-Wunderlich (HWW) syndrome. Methods: This study presents a rare case of hydronephrosis caused by UPJO due to crossing renal vessels, occurring concurrently with HWW syndrome at Military Hospital 175 from June 25 to July 24, 2024. Results: Contrast-enhanced computed tomography (CT) identified the obstruction caused by crossing vessels at the UPJ. The diagnosis of HWW was confirmed by magnetic resonance imaging (MRI). The patient underwent successful renal function-preserving treatment with retroperitoneal laparoscopic pyeloplasty and ureteral transposition. Conclusion: This case highlights the importance of early identification of the underlying cause of hydronephrosis in patients with a solitary kidney, such as those with HWW syndrome. Imaging modalities, especially contrast-enhanced CT, are valuable for detecting associated vascular anomalies.

Keywords

Herlyn-Werner-Wunderlich syndrome, Ureteropelvic junction obstruction, Crossing vessel

Article Details

References

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